Non-aneurysmal abdominal aortic rupture in a patient with Marfan syndrome

Eugene Ng1, Robert Tewksbury2, Andrew Mtl Choong3

  • 1Department of Vascular and Endovascular Surgery, Royal Brisbane and Women's Hospital, Herston, Queensland, Australia Discipline of Surgery, School of Medicine, University of Queensland, St. Lucia, Australia eugeneng82@gmail.com.

Insights

Non-aneurysmal aortic rupture is rare, often linked to penetrating atheromatous ulcers. This case highlights a unique instance in a Marfan syndrome patient, necessitating immediate surgical intervention over endovascular repair.

Area of Science:

  • Cardiovascular Surgery
  • Vascular Medicine
  • Genetics

Background:

  • Aortic rupture is commonly associated with aneurysmal disease.
  • Rupture of a non-aneurysmal aorta is a rare clinical event.
  • Penetrating atheromatous ulcers are the presumed cause of non-aneurysmal aortic rupture.

Observation:

  • A 68-year-old male with Marfan syndrome and prior aortic surgery presented with aortic rupture.
  • The patient had a non-aneurysmal aorta at the time of rupture.
  • The critical condition mandated immediate surgical hemorrhage control.

Findings:

  • This report details a rare case of aortic rupture in a non-aneurysmal aorta.
  • The patient's Marfan syndrome and surgical history are significant contributing factors.
  • Endovascular repair was not feasible due to the urgent need for hemostasis.

Implications:

  • This case expands the understanding of aortic rupture etiologies beyond aneurysmal disease.
  • It underscores the importance of considering non-aneurysmal rupture in specific patient populations.
  • Management strategies must prioritize rapid hemorrhage control in such critical scenarios.

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