Management of a Parturient with Diastrophic Dysplasia

Jacqueline S Lagoy1, Nathaniel D Kofford, Benoit J Gosselin

  • 1From the *Department of Anesthesiology, †Department of Otolaryngology, and ‡Department of Obstetrics and Gynecology, Dartmouth-Hitchcock Medical Center, Lebanon, New Hampshire; and §Mountain West Anesthesia, Park City, Utah.

A & a Case Reports
|July 1, 2015
PubMed

A 27-year-old primigravida patient with diastrophic dysplasia (DTD) presented to our obstetrics clinic at 8 weeks' gestational age. Diastrophic dysplasia is a rare, autosomal-recessive abnormality that presents multiple challenges to perinatal anesthetic management, including difficult airway management and relative contraindications to neuraxial anesthesia. The patient underwent elective cesarean delivery at 35 weeks' gestational age under general anesthesia. In this report, we describe our preoperative evaluation and management strategy that involved a multidisciplinary care team.

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