Simultaneous Repair of Right-Sided Coarctation and Vascular Ring
Joseph Herbert1, Francisco A Guzmán-Pruneda2, Elizabeth E Sumner2
1The University of Texas Medical School, Houston, Texas; Division of Congenital Heart Surgery, Texas Children's Hospital, and Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, Texas.
Abstract:
We present the case of a 4-year old girl with posterior fossa-hemangioma-arterial lesions-cardiac abnormalities/coarctation-eye abnormalities (PHACE) syndrome, an atypical, long-segment, right-sided coarctation of the aorta and vascular ring secondary to an aberrant left subclavian artery and left ligamentum. Simultaneous repair of both lesions was accomplished using a novel technique that included reimplantation of the aberrant left subclavian artery and translocation of the descending aorta to the proximal ascending aorta.
