[Arrhythmogenic dysplasia of the right ventricle]

The authors describe a case of sudden death of a 22-year-old man where on necropsy arrhythmogenic dysplasia of the right ventricle was found. The authors describe the clinical and morphological picture of this recent nosological unit. They discuss its relationship with Uhl's anomaly. Attention is drawn to concurrent affection of the left ventricle.