Is STEP the future for patients requiring proctocolectomy? A new therapeutic proposal from pediatric experience

Hansraj Mangray1, Fernando Ghimenton1

  • 1Department of Paediatric Surgery, Greys Hospital Pietermaritzburg, South Africa.

Clinical Case Reports
|August 15, 2015
PubMed

Insights

Juvenile colonic polyposis can be medically unmanageable. Serial transverse enteroplasties (STEP) of the distal ileum effectively controlled stooling in a pediatric patient after extensive surgery.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Colorectal Surgery

Background:

  • Juvenile colonic polyposis is a rare condition often requiring surgical intervention.
  • Medically refractory cases present significant management challenges.

Observation:

  • A pediatric patient with medically unmanageable juvenile colonic polyposis underwent subtotal colectomy with ileostomy, followed by proctectomy and ileal-J-pouch formation.
  • The patient also received serial transverse enteroplasties (STEP) of the distal ileum.

Findings:

  • The STEP procedure, when performed over an adequate length of the distal ileum, successfully managed the patient's stooling issues.
  • This surgical approach offered a solution for intractable polyposis.

Implications:

  • Serial transverse enteroplasties (STEP) represent a viable surgical option for managing complex cases of juvenile colonic polyposis.
  • This case highlights the potential of STEP in improving quality of life for pediatric patients with severe gastrointestinal polyposis.