[Leiomyosarcoma of the spermatic cord]

The case of leiomyosarcoma of the spermatic cord in a 54 year old man is reported. The patient was treated by surgical orchiepididymectomy and funnilectomy. After a review of the literature, the clinical and anatomopathological feature of this rare tumour and the surgical approach to it are discussed. The patient has had no recurrences and is still alive 16 months after surgery.