[Ileo-caeco-appendicular agenesis. 1 case]

A case of congenital absence of the appendix is reported. A 16 old years Female patient presented a 2 yr history peri-umbilical and hypogastric pain with tenderness in the right lower quadrant. Abdominal radiography and echography were normal. Exploration through a Mc Burney incision found only small intestine. After midline incision, mesenterium commun and agenesis of vermiform appendix were found. Abnormal adhesions of right quadrant were divided. The post-operative course was uncomplicated. Absence of the appendix is a very rare condition. This diagnosis should not be made unless the ileocecal area is thoroughly explored. Only the laparoscopy could achieve diagnosis before surgery.