[Congenital coronary arteriovenous fistula: analysis of five cases]

Zhonghua Minguo Xiao Er Ke Yi Xue Hui Za Zhi [Journal]. Zhonghua Minguo Xiao Er Ke Yi Xue Hui
|March 1, 1989
PubMed

Insights

Congenital coronary arteriovenous fistula, a rare heart defect, can be safely treated with surgery. Early surgical correction is recommended for patients with significant shunts or symptoms.

Area of Science:

  • Cardiology
  • Pediatric Cardiac Surgery
  • Congenital Heart Disease

Background:

  • Congenital coronary arteriovenous fistula (ccAVF) is a rare anomaly where coronary arteries connect directly to heart chambers or major vessels.
  • Diagnosis typically involves non-invasive (echocardiogram) and invasive (cardiac catheterization, angiocardiography) methods.
  • ccAVF can lead to significant hemodynamic alterations and clinical manifestations, necessitating timely intervention.

Observation:

  • A study reviewed 5 pediatric patients (3 months to 13 years) diagnosed with ccAVF between 1982 and 1988.
  • Presentations varied from asymptomatic to symptomatic, including congestive heart failure, exertional dyspnea, and fatigue.
  • All patients exhibited a right coronary arteriovenous fistula draining into the right ventricle, with characteristic murmur findings.

Findings:

  • All five patients underwent successful surgical correction for their ccAVF.
  • Surgical techniques included direct epicardial ligation, cardiopulmonary bypass with direct suture closure, and Dacron patch closure.
  • No postoperative complications were reported, indicating a high safety profile for surgical intervention.

Implications:

  • Surgical correction of congenital coronary arteriovenous fistula is a safe and effective treatment option.
  • Early surgical intervention should be considered for pediatric patients with ccAVF, especially those with significant shunts or clinical symptoms.
  • This study highlights the long-term safety and efficacy of surgical management for ccAVF in a pediatric cohort.