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Problems of patients with cystic fibrosis during transition to adulthood

Violetta Opoka-Winiarska1, Szczepan Cofta, Henryk Mazurek

  • 1Department of Paediatric Pulmonology and Rheumatology, Medical University of Lublin, Poland. ftpulmza@sum.edu.pl.

Pneumonologia I Alergologia Polska
|September 18, 2015
PubMed

Insights

Cystic fibrosis (CF) care requires lifelong management, focusing on a crucial transition from pediatric to adult internal medicine. Specialized care centers improve longevity and quality of life for adult CF patients.

Area of Science:

  • Pulmonology
  • Internal Medicine
  • Pediatrics

Background:

  • Cystic fibrosis (CF) is a lifelong genetic disorder requiring continuous medical management.
  • A significant mortality rate exists for CF patients before reaching adulthood.
  • Effective transition from pediatric to adult care is critical for CF patient outcomes.

Purpose of the Study:

  • To review essential elements of lifelong care for cystic fibrosis patients.
  • To highlight the importance of a structured transition process from pediatric to adult internal medicine.
  • To emphasize the need for specialized adult care centers for CF exacerbations.

Main Methods:

  • Literature review on cystic fibrosis patient care pathways.
  • Analysis of transition challenges from pediatric to adult healthcare settings.
  • Examination of the impact of specialized CF care teams on patient outcomes.

Main Results:

  • Successful transition requires more than medical record transfer; it necessitates patient preparation and education.
  • Adult CF patients benefit significantly from specialized care centers, improving survival and quality of life.
  • While pediatric CF care transition is addressed, adult CF care models require further development.

Conclusions:

  • Lifelong, specialized care is paramount for individuals with cystic fibrosis.
  • A well-prepared transition to adult internal medicine and access to expert centers are key to optimizing CF patient health.
  • Further development of adult-focused CF care strategies is essential.

Keywords:
childhood to adulthoodcystic fibrosis

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