Adrenal incidentaloma caused by extramedullary haematopoiesis: conservative management is optimal

Suganya Sekar1, Deepak Burad2, Aby Abraham3

  • 1Department of Endocrine Surgery, Christian Medical College, Vellore, Tamil Nadu, India.

BMJ Case Reports
|September 23, 2015
PubMed

We present a thalassaemic patient with extramedullary haematopoiesis in the adrenal gland, which is one of the rare sites of involvement. A 29-year-old man presented with a history of anaemia since childhood which required blood transfusion recently. On examination, he had pallor, icterus and splenomegaly with no other palpable abdominal mass. He was diagnosed to have β-thalassaemia. Ultrasonography of the abdomen showed an incidental right adrenal mass with splenomegaly; CT revealed a large right adrenal mass with heterogeneous density. Adrenal adenoma, carcinoma and extramedullary haematopoiesis were considered in the differential diagnosis. After excluding a functioning tumour, the diagnosis was confirmed by ultrasound-guided biopsy. Since the patient was asymptomatic, the adrenal lesion was managed conservatively.

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