[Beckwith-Wiedemann syndrome. Presentation of a clinical case]

The interest we see in oral pathology about Beckwith-Wiedemann syndrome is not strictly related to the association with neoplasms of the syndrome but, first of all, to the high frequency of macroglossia in the patients affected. In fact this pathologic situation, setting up since birth, can strongly modify the growth of teeth and facial skeleton. Therapy consists in a partial glossectomy. After this reducing is advised a contention applied to the chin.