Fibromuscular Dysplasia of Renal and Carotid Arteries

Denisa Jahnlova1, Josef Veselka1

  • 1Department of Cardiology, Charles University in Prague, 2nd Faculty of Medicine and Motol University Hospital, Prague, Czech Republic.

Insights

Fibromuscular dysplasia (FMD) can affect various arteries, leading to conditions like hypertension or stroke. Early diagnosis and appropriate treatment, such as angioplasty for renal artery stenosis, are crucial for managing FMD.

Area of Science:

  • Vascular Medicine
  • Radiology

Background:

  • Fibromuscular dysplasia (FMD) is a rare, non-atherosclerotic, non-inflammatory condition affecting arterial walls.
  • It can impact multiple arterial beds, including renal and carotid arteries.

Observation:

  • Two cases of FMD are presented: an asymptomatic 75-year-old man with carotid artery FMD and a 17-year-old male with renal artery FMD causing hypertension.
  • The latter case was successfully treated with angioplasty.

Findings:

  • FMD can manifest as arterial hypertension (renal artery involvement) or cerebrovascular events like stroke or transient ischemic attack (carotid/vertebral artery involvement).
  • Many FMD cases are asymptomatic and incidentally discovered.

Implications:

  • Percutaneous transluminal angioplasty is recommended for renal artery stenosis causing hypertension.
  • Conservative management is advised for asymptomatic, extensive carotid artery FMD lesions.

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