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The anticardiolipin syndrome.
1Cleveland Clinic Foundation, Ohio.
American Family Physician
|January 1, 1989
Summary
Anticardiolipin antibodies are linked to a syndrome causing blood clots, low platelets, and pregnancy loss, often with autoimmune disorders. Diagnosis is improving with new tests, but treatments like prednisone and aspirin remain debated.
Area of Science:
- Immunology
- Hematology
- Obstetrics & Gynecology
Background:
- Anticardiolipin antibodies are associated with a distinct clinical syndrome.
- This syndrome involves venous and arterial thrombosis, thrombocytopenia, and recurrent fetal loss.
- Autoimmune diseases frequently accompany this condition.
Purpose of the Study:
- To describe the characteristics of anticardiolipin antibody syndrome.
- To highlight the availability of a standardized diagnostic test.
- To discuss current and potential treatment strategies.
Main Methods:
- Utilizes a standardized enzyme immunoassay for anticardiolipin antibody detection.
- Reviews existing literature on clinical manifestations and treatment outcomes.
- Analyzes patient data related to thrombosis and fetal loss.
Main Results:
- A standardized enzyme immunoassay for anticardiolipin antibodies is now widely available.
- Treatment strategies, particularly for pregnant patients, are controversial.
- Prednisone and aspirin are used in pregnant patients; anticoagulation is recommended for thrombosis.
Conclusions:
- Anticardiolipin antibody syndrome is a significant clinical entity requiring further research.
- Standardized testing aids in diagnosis and management.
- Optimal treatment protocols, including the role of plasmapheresis and cytotoxic agents, require further investigation.