Partial and intermediate atrioventricular septal defects without major associated cardiac anomalies

Area of Science:

• Cardiology
• Pediatric Cardiac Surgery

Background:

• Partial and intermediate atrioventricular septal defects (p-i AVSDs) represent 20-40% of all atrioventricular septal defects.
• Children with p-i AVSDs are often asymptomatic, with surgery typically performed before preschool age or earlier if heart failure develops.

Purpose of the Study:

• To review current surgical management options and outcomes for p-AVSD and i-AVSD variants.
• Focus on cases without major associated cardiac malformations.

Main Methods:

• Review of surgical techniques and outcomes for p-i AVSD repair.
• Analysis of long-term results, including mortality, reoperation rates, and morbidity.

Main Results:

• Surgical repair of p-i AVSDs has demonstrated success for over six decades.
• Outcomes have significantly improved over the past 50 years, with reduced mortality.
• Despite improvements, reoperation and long-term morbidity remain concerns for some patients.

Conclusions:

• Surgical management of p-i AVSDs has evolved, offering improved results.
• Continued focus on minimizing reoperations and addressing long-term morbidity is essential for optimal patient care.