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Rare Presentation of Lupus Myocarditis With Acute Heart Failure-A Case Report
Gurveen Malhotra1, Serafin Chua, Vamsi Kodumuri
1Departments of 1Internal Medicine; 2Rheumatology; 3Cardiology; 4Pulmonary and Critical Care Medicine; and 5Family Medicine, Mt Sinai Hospital, Chicago, IL.
Abstract:
Systemic lupus erythematosus is an autoimmune disease with diffuse organ involvement. The cardiac complications include pericarditis, myocarditis, pulmonary hypertension, coronary vasculitis, and Libman-Sacks endocarditis. Symptomatic lupus myocarditis presenting with left ventricular dysfunction, acute heart failure, and pulmonary edema, although rare, is a life-threatening complication. We report the occurrence of acute lupus myocarditis in a 38-year-old postpartum female who had a cesarean section a week before presentation for preeclampsia. Initially she was managed for pneumonia but later found to have acute pericarditis and myocarditis related to systemic lupus erythematosus. She had a complicated hospital course including acute respiratory failure and cardiogenic shock. She was started on pulse dose steroids besides the treatment for heart failure and had a dramatic improvement within days.
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