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Left Atrial Stenosis Induced Pulmonary Venous Arterialization and Group 2 Pulmonary Hypertension in Rat
Published on: November 18, 2018
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Left isomerism syndrome with total anomalous systemic connection
Anh Tuan Vo1, Khang Dang Cao1, Khoi Minh Le1
1Department of Cardiovascular Surgery, University Medical Center, University of Medicine and Pharmacy in Ho Chi Minh City, Ho Chi Minh City, Vietnam.
Asian Cardiovascular & Thoracic Annals
|November 28, 2015
Summary
This study details a rare case of left isomerism with abnormal systemic venous connection, successfully treated with complete surgical repair. The findings highlight effective diagnostic and treatment strategies for this complex congenital heart defect.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Left isomerism, a rare congenital anomaly, presents complex cardiac malformations.
- Total anomalous systemic venous connection (TASVC) involves abnormal drainage of systemic veins.
Observation:
- A 7-year-old patient presented with absent inferior vena cava and other systemic veins abnormally connected to the left atrium.
- The condition included a hypoplastic right atrium, intact atrial septum, and pulmonary blood flow via a ventricular septal defect.
Findings:
- Diagnosis was confirmed using echocardiography, angiography, and computed tomography.
- Complete surgical repair was successfully performed, addressing the complex venous anomalies and intracardiac defects.
Implications:
- This case demonstrates the feasibility of successful surgical correction for complex left isomerism with TASVC.
- Effective diagnostic imaging and surgical planning are crucial for favorable outcomes in such pediatric cardiac cases.
Keywords:
Heart atriaHeart defectsHeart septal defectsVascular malformationsVena cavaatrialcongenitalinferiorsuperiorMore Related Videos
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