Novel three-sinus enlargement technique for supravalvular aortic stenosis without aortic transection

Area of Science:

• Cardiovascular Surgery
• Pediatric Cardiology
• Congenital Heart Defects

Background:

• Supravalvular aortic stenosis (SVAS) repair can have high rates of residual stenosis, especially in complex forms.
• Surgical outcomes for complex SVAS remain a challenge in pediatric cardiac surgery.

Observation:

• A 6-month-old infant diagnosed with aortic valve stenosis (AS) at 1 month of age presented with moderate AS and discrete sino-tubular junction stenosis.
• Diagnostic imaging, including echocardiography and cardiac catheterization, confirmed the stenosis of the proximal ascending aorta.

Findings:

• A novel reconstructive operation involving three-sinus and ascending aorta enlargement was performed without aortic root transection.
• This technique was successfully applied to a 6-month-old infant weighing less than 10 kg.

Implications:

• The novel three-sinus enlargement technique is a viable treatment for all types of SVAS in infants.
• This method is particularly beneficial for low-weight infants, promoting normal ascending aorta growth post-surgery.