Killing Me Softly: Connotations to Unfolded Protein Response and Oxidative Stress in Alzheimer's Disease

Beata Pająk1, Elżbieta Kania2, Arkadiusz Orzechowski1

  • 1Electron Microscopy Platform, Mossakowski Medical Research Centre, Polish Academy of Sciences, Pawińskiego 5, 02-106 Warsaw, Poland; Department of Physiological Sciences, Faculty of Veterinary Medicine, Warsaw University of Life Sciences (SGGW), Nowoursynowska 159, 02-776 Warsaw, Poland.

Insights

Mitochondrial dysfunction in Alzheimer's disease (AD) is linked to altered lipid metabolism and protein processing. APP, Aβ, and tau accumulation in mitochondria disrupt cellular energy production, leading to neuronal loss.

Area of Science:

  • Neuroscience
  • Mitochondrial Biology
  • Biochemistry

Background:

  • Mitochondrial dysfunction is a key feature of Alzheimer's disease (AD).
  • The precise mechanisms linking protein processing and lipid metabolism to mitochondrial pathology in AD are not fully understood.

Purpose of the Study:

  • To review the causes and molecular mechanisms of mitochondrial dysfunction in AD.
  • To explore the consequences of amyloid precursor protein (APP), amyloid-beta (Aβ), and tau in mitochondria.
  • To investigate the role of altered lipid metabolism in AD pathogenesis.

Main Methods:

  • Literature review focusing on molecular mechanisms and cellular processes.
  • Analysis of the role of protein translocation, posttranslational modifications, and lipid metabolism.
  • Examination of the impact on mitochondrial biochemistry, bioenergetics, and oxidative stress.

Main Results:

  • APP, Aβ, and tau proteins accumulate in mitochondria, impairing protein import and oxidative phosphorylation.
  • Metabolic disturbances, particularly in geranylgeraniol metabolism, affect protein glycosylation and folding.
  • Mitochondrial impairment leads to oxidative stress and ultimately neuronal apoptosis in AD.

Conclusions:

  • Altered lipid metabolism and aberrant protein processing contribute significantly to mitochondrial dysfunction in AD.
  • APP translocation to mitochondria disrupts essential cellular functions, exacerbating AD pathology.
  • Targeting mitochondrial pathways and lipid metabolism may offer therapeutic strategies for AD.

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