A Striking Coronary Artery Pattern in a Grown-Up Congenital Heart Disease Patient

Area of Science:

• Cardiology
• Developmental Biology
• Medical Imaging

Background:

• Left ventricular noncompaction (LVNC) is a myocardial disorder resulting from abnormal left ventricle development.
• LVNC can be isolated or accompanied by other cardiac and extracardiac anomalies, such as coronary artery anomalies.
• Despite advancements in imaging, LVNC diagnosis remains challenging, particularly when co-occurring with other heart conditions.

Purpose of the Study:

• To report a rare case of left ventricular noncompaction (LVNC).
• To describe the association of LVNC with malposition of the great arteries.
• To detail an unusual coronary artery pattern in a patient with LVNC.

Main Methods:

• Case report detailing clinical presentation and diagnostic findings.
• Review of medical literature on LVNC and associated anomalies.
• Advanced cardiac imaging techniques to elucidate cardiac and coronary anatomy.

Main Results:

• The patient presented with left ventricular noncompaction (LVNC).
• The case demonstrated a co-occurrence of LVNC with malposition of the great arteries.
• A highly original coronary artery pattern was identified in conjunction with LVNC.

Conclusions:

• Left ventricular noncompaction (LVNC) can present with complex congenital heart anomalies.
• Accurate diagnosis of LVNC requires high-resolution imaging, especially in the presence of other cardiac pathologies.
• This case underscores the importance of recognizing diverse presentations of LVNC and its associated vascular abnormalities.