Presumed bilateral cilioretinal artery occlusion related to relapsing white dot syndrome

To report a presumed case of bilateral asynchronous cilioretinal occlusion associated with white dot syndrome.

A 19-year-old woman presented with decreased vision in the right eye. Cilioretinal occlusion was diagnosed and multimodal imaging was performed.

Laboratory workup was negative. Fluorescein and indocyanine green angiography revealed an inflammatory choroidopathy in the right eye. Spectral-domain coherence tomography (OCT) initially showed internal retinal layer edema followed by atrophy in the papillomacular bundle. Left eye presented asymptomatic decreased visual acuity and OCT findings were compatible with previous cilioretinal occlusion.

Cilioretinal occlusion findings were present in both eyes. Multimodal fundus imaging allowed idiopathic inflammatory choroidopathy diagnosis in the right eye, suggesting that a recurrent inflammatory process caused an asynchronous vascular occlusion.