[Acute urinary retention caused by hematocolpos associated with uterus didelphys and ipsilateral renal agenesis]

Acute urinary retention from compressive hematocolpos is an uncommon form of presentation of the multi-malformation syndrome arising from failed fusion of the Müllerian ducts and is characterized by uterus didelphys, vaginal duplication (one with hematocolpos), and unilateral renal agenesis. A case is reported and the literature reviewed.