Cor triatriatum dexter: A rare cause of cyanosis during neonatal period

Mohammed Hussien Alghamdi1

  • 1Department of Cardiac Science, College of Medicine, King Saud University, Riyadh, Kingdom of Saudi Arabia.

Insights

Cor-triatriatum dexter, a rare congenital heart defect, partitions the right atrium. Surgical resection of the dividing membrane successfully treated a neonate with cyanosis.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Cor-triatriatum dexter is an extremely rare congenital heart defect.
  • It involves the persistence of the right valve of the embryonic sinus venosus, partitioning the right atrium.
  • This partitioning creates distinct smooth and trabeculated portions within the atrium.

Observation:

  • A 1-week-old infant presented with intermittent central cyanosis.
  • Diagnosis was confirmed via echocardiography and bubble contrast study.
  • The defect was isolated, with no other cardiac abnormalities.

Findings:

  • Initial treatment with cardiac catheterization failed to disrupt the membrane.
  • Successful treatment was achieved through open-heart surgery to resect the cor-triatriatum dexter membrane.
  • The surgical outcome was uncomplicated.

Implications:

  • This case highlights the challenges in managing cor-triatriatum dexter.
  • Surgical intervention remains a definitive treatment option for this rare condition.
  • Early diagnosis and appropriate management are crucial for improving outcomes in affected neonates.

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