Pulmonary Epithelioid Hemangioendothelioma Diagnosed With Endobronchial Biopsies: A Case Report and Literature Review
Kenneth K Sakata1, Michael B Gotway, Maxwell L Smith
1*Division of Pulmonary Medicine ‡Department of Laboratory Medicine and Pathology ∥Division of Hematology and Oncology, Mayo Clinic, Scottsdale †Department of Radiology §Division of Hospital Internal Medicine, Mayo Clinic Hospital, Phoenix, AZ.
Abstract:
Pulmonary epithelioid hemangioendothelioma (PEHE) is a rare vascular tumor of endothelial origin first described in 1975 as intravascular bronchioloalveolar tumor. Since then, >100 cases have been reported, and most cases require surgical lung biopsy for diagnosis. We report the case of a 46-year-old man with a diagnosis of PEHE from endobronchial biopsies of an intraluminal nodule, a rare presentation of this disease. We summarize a review of the literature and the bronchoscopic findings of PEHE.
