Pulmonary alveolar microlithiasis with finger clubbing: A case report and literature review

Xin Qian1, Xiaofeng Wu1, Xianjun Liu1

  • 1Department of Respiratory Medicine, Shiyan Taihe Hospital, Hubei University of Medicine, Shiyan, Hubei 442000, P.R. China.

Insights

Pulmonary alveolar microlithiasis (PAM) is a rare genetic lung disease. Early diagnosis via bronchoalveolar lavage fluid examination and imaging is key for managing this condition.

Area of Science:

  • Pulmonology
  • Genetics
  • Radiology

Background:

  • Pulmonary alveolar microlithiasis (PAM) is a rare, slowly progressive autosomal recessive lung disease.
  • Mutations in the solute carrier family 34, member 2 gene are implicated in PAM.
  • Consanguinity, particularly parental cousin relationships, is frequently observed in PAM patients.

Purpose of the Study:

  • To report a case of Pulmonary alveolar microlithiasis (PAM) in a 35-year-old female.
  • To detail the clinical, radiological, and pathological findings of PAM.
  • To review current knowledge and propose diagnostic methods for PAM.

Main Methods:

  • Case report of a 35-year-old female diagnosed with PAM.
  • Pulmonary function tests (PFTs) to assess ventilatory and diffusion defects.
  • High-resolution computed tomography (HRCT) for imaging calcifications.
  • Bronchoalveolar lavage fluid (BALF) analysis and transbronchial biopsy for pathological confirmation.

Main Results:

  • The patient presented with restrictive ventilatory and diffusion defects.
  • HRCT revealed diffuse ground-glass opacities and subpleural calcifications.
  • BALF and biopsy confirmed numerous, concentrically laminated calcified bodies characteristic of PAM.
  • Inhaled corticosteroid treatment led to symptom improvement.

Conclusions:

  • PAM diagnosis can be supported by characteristic radiological findings and confirmed via BALF examination.
  • Early identification and management of PAM are crucial.
  • Further research into the genetic basis and treatment of PAM is warranted.

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