[Subtotal cor triatriatum sinister associated with bilateral partial anomalous pulmonary venous return]

Onur Işık1, Muhammet Akyüz2, Mehmet Fatih Ayık1

  • 1Department of Cardiovascular Surgery, Ege University Faculty of Medicine, İzmir, Turkey.

Insights

Cor triatriatum sinister, a rare congenital heart defect, involves an extra chamber dividing the left atrium. This case highlights a subtotal form with anomalous pulmonary venous return in an infant.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Pediatric Cardiology

Background:

  • Cor triatriatum sinister is a rare congenital cardiac anomaly, accounting for 0.1% of all such defects.
  • It is frequently associated with other complex cardiac malformations.
  • The condition involves an accessory chamber within the left atrium that obstructs pulmonary venous return.

Observation:

  • A case report of a 4-month-old male infant is presented.
  • The patient exhibited subtotal cor triatriatum sinister.
  • Associated anomalies included right and left upper anomalous pulmonary venous return.

Findings:

  • The patient presented with a specific anatomical variant of cor triatriatum sinister.
  • The anomalous pulmonary venous return further complicated the cardiac physiology.
  • Surgical or interventional management strategies would depend on the precise anatomical details and hemodynamic impact.

Implications:

  • This case underscores the importance of detailed imaging in diagnosing complex congenital heart defects.
  • Understanding rare variants like subtotal cor triatriatum sinister is crucial for effective clinical management.
  • Such cases contribute to the broader knowledge base for treating pediatric cardiac anomalies.

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