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Functional Class in Children with Idiopathic Dilated Cardiomyopathy. A pilot Study
Aline Cristina Tavares1, Edimar Alcides Bocchi1, Guilherme Veiga Guimarães1
1Instituto do Coração, Hospital Sírio-libanês, São Paulo, SP, Brazil.
Arquivos Brasileiros De Cardiologia
|May 12, 2016
Summary
Children with idiopathic dilated cardiomyopathy (IDCM) can use drawings for self-classification of functional capacity. This self-classification correlates with medical assessments and Weber's stratification, aiding in understanding their condition.
Area of Science:
- Pediatric Cardiology
- Cardiovascular Research
- Clinical Assessment
Background:
- Idiopathic dilated cardiomyopathy (IDCM) is a leading cause of death in children.
- Low left ventricular ejection fraction (LVEF) and functional capacity (FC) are key mortality indicators.
- Children cannot reliably self-report their functional capacity.
Purpose of the Study:
- To determine if children's, parents', and medical staff's functional capacity classifications align.
- To investigate the correlation between VO2 max and Weber's classification in pediatric IDCM patients.
Main Methods:
- Prepubertal children diagnosed with IDCM and heart failure (HF) were evaluated.
- Cardiopulmonary exercise testing (CPET) and functional class assessments were performed.
- Statistical analyses, including Chi-square tests, were used to compare classifications.
Main Results:
- A significant association was found between medical staff (CFm) and parent (CFp) functional classifications (p=0.002).
- No significant associations were observed between parent (CFp) and child (CFc) classifications, or between medical staff (CFm) and child (CFc) classifications.
- Weber's classification showed significant correlations with medical staff (CFm), parent (CFp), and child (CFc) classifications (p<0.05).
Conclusions:
- Utilizing drawings facilitated children's self-classification of functional capacity (NYHA).
- Children's self-classification, aided by drawings, correlated with Weber's stratification.
- This approach may improve the understanding of functional status in pediatric IDCM.
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