Implantable cardioverter-defibrillators in congenital heart disease

H Chubb1,2, E Rosenthal3,4

  • 1Department of Paediatric Cardiology, Evelina London Children's Hospital, Westminster Bridge Road, SE1 7EH, London, UK.

Insights

Implantable cardioverter-defibrillators (ICDs) can prevent sudden cardiac death in congenital heart disease (CHD) patients. Careful consideration of risks, benefits, and patient factors is crucial for optimal ICD strategy and long-term management.

Area of Science:

  • Cardiology
  • Medical Devices

Background:

  • Implantable cardioverter-defibrillators (ICDs) are vital for preventing sudden cardiac death (SCD) in patients with congenital heart disease (CHD).
  • Evaluating the risks and benefits of ICDs in the diverse CHD population presents unique challenges.
  • A personalized approach is essential for effective ICD implantation and management in CHD patients.

Purpose of the Study:

  • To review primary and secondary indications for ICD implantation in CHD patients.
  • To discuss implantation techniques and long-term follow-up strategies for ICDs in this population.
  • To highlight recent findings on system longevity, lead extraction, inappropriate shocks, and quality of life.

Main Methods:

  • This review synthesizes information from recent publications and clinical guidelines.
  • It focuses on risk stratification and patient-specific factors for tailored ICD strategies.
  • The review examines challenges in managing ICDs in the heterogeneous CHD population.

Main Results:

  • ICDs play a significant role in reducing SCD in CHD patients.
  • Adverse effects, including system longevity issues and lead complications, require careful evaluation.
  • Inappropriate shocks and impact on quality of life are critical considerations for long-term management.

Conclusions:

  • A tailored approach considering individual risk factors and patient-specific characteristics is necessary for ICD selection in CHD.
  • Long-term follow-up must address system longevity, lead issues, shock burden, and quality of life.
  • Careful consideration of all factors is paramount before committing to ICD therapy in CHD patients.

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