Related Experiment Video
Updated: Mar 19, 2026

04:34
Surgical Treatment of an Endolymphatic Sac Tumor
Published on: May 26, 2023
1.8K
Primary pericranial Ewing's sarcoma on the temporal bone: A case report.
Hiroto Kawano1, Naoki Nitta1, Mitsuaki Ishida2
1Department of Neurosurgery. Shiga University of Medical Science, Setatsukinowa-cho, Shiga, Japan.
Surgical Neurology International
|June 17, 2016
Summary
A rare case of pericranial Ewing's sarcoma, a primary bone cancer on the temporal bone, is presented. This extremely rare tumor occurred in a 9-year-old female patient.
Area of Science:
- Oncology
- Orthopedic Oncology
- Pediatric Oncology
Background:
- Primary Ewing's sarcoma is exceptionally rare when originating in the pericranium.
- The pericranium, the outermost layer of the skull, is an unusual site for this type of bone cancer.
Purpose of the Study:
- To report an extremely rare case of primary Ewing's sarcoma arising from the pericranium.
- To introduce a new classification: "pericranial Ewing's sarcoma" for tumors located in this specific sub-periosteal location.
Main Methods:
- Case presentation of a 9-year-old female with a left temporal subcutaneous mass.
- Diagnostic imaging included head computed tomography (CT), F-18 fluorodeoxyglucose positron emission tomography (FDG-PET), and magnetic resonance imaging (MRI).
- Surgical resection of the mass and involved temporal bone, followed by histopathological diagnosis.
Main Results:
- Imaging revealed a temporal bone mass with bony spicules, without bone destruction or intracranial invasion.
- The mass was situated between the temporal bone and the pericranium.
- Histopathology confirmed the diagnosis of primary Ewing's sarcoma, classified as pericranial Ewing's sarcoma due to its location.
Conclusions:
- This case represents an extremely rare instance of primary pericranial Ewing's sarcoma.
- The proposed classification of "pericranial Ewing's sarcoma" aids in describing tumors in this unique anatomical site.

