Ewing Sarcoma of the External Ear Canal

Area of Science:

• Oncology
• Pediatric Oncology
• Surgical Pathology

Background:

• Ewing sarcoma (ES) is a high-grade malignant tumor with skeletal and extraskeletal forms.
• Extraskeletal ES commonly affects the head and neck but has not been previously reported in the external ear canal.
• This study presents a rare case of extraskeletal ES in a pediatric patient's external ear canal.

Purpose of the Study:

• To report a unique case of extraskeletal Ewing sarcoma originating in the external ear canal.
• To emphasize the diagnostic challenge posed by extraskeletal ES mimicking common conditions.

Main Methods:

• Surgical resection of the tumor.
• Adjuvant chemotherapy using a VAC/IE (vincristine, adriamycin, cyclophosphamide alternating with ifosfamide, and etoposide) regimen for 12 months.
• Clinical presentation and diagnostic workup of a 2-year-old boy.

Main Results:

• A 2-year-old boy was diagnosed with extraskeletal ES of the external ear canal.
• The tumor initially mimicked an auricular hematoma.
• Successful surgical management and 12-month adjuvant chemotherapy were completed.

Conclusions:

• Extraskeletal Ewing sarcoma should be considered in the differential diagnosis of head and neck tumors.
• Nonspecific clinical presentations can mask serious conditions like ES.
• Early consideration of rare diagnoses is crucial for appropriate patient management.