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Adult Hirschsprung's disease
W T Hung1, T P Chiang, Y W Tsai
1Department of Surgery, National Taiwan University Hospital, Taipei, Republic of China.
Journal of Pediatric Surgery
|April 1, 1989
Summary
Adult Hirschsprung's disease presents unique challenges compared to pediatric cases. This study details 17 adult patients, highlighting distinct symptoms, diagnostic criteria, and surgical outcomes for this rare condition.
Area of Science:
- Gastroenterology
- Colorectal Surgery
- Pediatric Surgery
Background:
- Hirschsprung's disease is typically diagnosed in infancy.
- Adult presentation of Hirschsprung's disease is uncommon and may differ significantly from pediatric cases.
- Understanding adult Hirschsprung's disease is crucial for accurate diagnosis and effective management.
Purpose of the Study:
- To describe the clinical characteristics of adult Hirschsprung's disease.
- To analyze diagnostic criteria and operative findings in adult patients.
- To review surgical procedures and outcomes for adult Hirschsprung's disease.
Main Methods:
- Retrospective case series analysis.
- Review of 17 adult patients treated between 1965 and 1988.
- Analysis of patient symptoms, diagnostic methods, and surgical interventions.
Main Results:
- Adult Hirschsprung's disease exhibits distinct clinical presentations.
- Diagnostic challenges exist in adult cases.
- Surgical approaches vary based on individual patient findings.
Conclusions:
- Adult Hirschsprung's disease requires tailored diagnostic and therapeutic strategies.
- Further research is needed to optimize management for this patient population.
- Early recognition and appropriate surgical intervention are key to favorable outcomes.