Gastrointestinal Manifestations of Cystic Fibrosis
1Dr Sabharwal is an attending staff physician and instructor in pediatrics in the Division of Gastroenterology and Nutrition at Harvard Medical School in Boston, Massachusetts. She is also an attending gastroenterologist at the Cystic Fibrosis Center in Boston Children's Hospital in Boston, Massachusetts.
Abstract:
Cystic fibrosis has historically been considered a pulmonary disease, but with the increasing life expectancy of these patients, gastrointestinal manifestations are becoming more important. Furthermore, nutritional status is closely linked to pulmonary function and, thus, overall mortality. This article discusses gastrointestinal manifestations (which involve nutritional, pancreatic, hepatobiliary, and, in particular, gastrointestinal tract issues) of cystic fibrosis as well as management of the disease. In addition, the article discusses studies that have been critical to our understanding of gastrointestinal manifestations of cystic fibrosis.
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