A rare pathology: Levoatriocardinal vein

Öykü Tosun1, Murat Saygı2, Taner Kasar2

  • 1Department of Pediatric Cardiology, Mehmet Akif Ersoy Cardiovascular Training and Research Hospital, İstanbul, Turkey. isaltosun@hotmail.com.

Insights

Levoatriocardinal vein (LACV) is a rare cardiac anomaly, often linked to left-sided obstructive lesions. This study reviews 11 cases, highlighting diagnostic echocardiographic views and clinical presentations.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Levoatriocardinal vein (LACV) is a rare congenital anomaly connecting the pulmonary venous and cardinal systems.
  • It is infrequently encountered and often associated with other cardiac defects.

Purpose of the Study:

  • To describe the morphological and clinical characteristics of LACV.
  • To outline diagnostic methods for identifying LACV.
  • To review institutional experience with LACV cases.

Main Methods:

  • Retrospective review of 11 patients diagnosed with LACV between 2010 and 2014.
  • Echocardiography was the primary diagnostic tool to confirm LACV presence and assess associated lesions.
  • Evaluation included identification of left-sided obstruction and interatrial septum integrity.

Main Results:

  • 82% of patients were diagnosed under one year of age.
  • Nine patients presented with left-sided obstruction; two had normal intracardiac anatomy.
  • Echocardiography in specific views confirmed LACV originating from the left atrium in all cases.

Conclusions:

  • LACV is extremely rare and predominantly occurs with left-sided obstructive lesions.
  • Consideration of LACV is crucial in patients with left-sided obstructions.
  • LACV can also manifest in individuals with normal intracardiac anatomy and pulmonary venous return.
Abstract

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