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Transcellular transport and membrane insertion of the C5b-9 membrane attack complex of complement by glomerular

D Kerjaschki1, M Schulze, S Binder

  • 1Institute of Pathological Anatomy, University of Vienna, Austria.

Insights

The C5b-9 complex is crucial for membranous nephropathy (MN) and proteinuria. In passive Heymann nephritis (PHN), C5b-9 inserts into glomerular epithelial cells (GEC) and is endocytosed, protecting GEC from damage.

Area of Science:

  • Nephrology
  • Immunology
  • Cell Biology

Background:

  • Deposition of the C5b-9 complement complex in glomeruli is essential for proteinuria development in experimental membranous nephropathy (MN).
  • Understanding the precise localization and cellular handling of C5b-9 in MN is critical for developing targeted therapies.

Purpose of the Study:

  • To investigate the distribution and cellular fate of the C5b-9 complex in passive Heymann nephritis (PHN), a model of MN.
  • To compare C5b-9 localization in PHN with another MN model induced by cationic human IgG.

Main Methods:

  • Immunoelectron microscopy using a mAb specific for the C5b-9(m) neoantigen.
  • Freeze-fracture electron microscopy to identify intramembrane particles.
  • Immunoblotting of rat urine to detect C5b-9 degradation products.

Main Results:

  • In PHN, C5b-9 was found in immune deposits and on glomerular epithelial cell (GEC) membranes, particularly in clathrin-coated pits and vesicles.
  • C5b-9 was concentrated in multivesicular bodies within GEC and associated with urinary vesicles, suggesting exocytosis.
  • In contrast, C5b-9 was primarily in immune deposits in the cationic IgG-MN model, with rare intracellular localization in GEC.
  • Freeze-fracture revealed particles resembling membrane-inserted C5b-9(m) in GEC foot process membranes in PHN.
  • Degradation products of C5b-9 were detected in PHN rat urine.

Conclusions:

  • In PHN, C5b-9 is inserted into GEC membranes.
  • GEC selectively endocytose and transport membrane-inserted C5b-9 via a vesicular mechanism.
  • This cellular transport protects GEC from the accumulation of membrane-inserted C5b-9, mitigating cellular damage.

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