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Kasabach - Merritt syndrome: A case report
1Paediatric and Child health Department , Omdurman Islamic University. Omdurman , Sudan.
Sudanese Journal of Paediatrics
|August 6, 2016
Summary
Kasabach-Merritt syndrome involves vascular tumors and blood clotting issues. This case highlights a rare presentation in a Saudi infant with bleeding symptoms.
Area of Science:
- Pediatric Hematology
- Vascular Anomalies
- Coagulation Disorders
Background:
- Kasabach-Merritt syndrome (KMS) is a rare condition.
- It is characterized by a vascular tumor, thrombocytopenia, microangiopathic hemolytic anemia, and consumptive coagulopathy.
- The syndrome arises from platelets and clotting factors being consumed within the tumor.
Observation:
- A two-and-a-half-month-old Saudi female infant presented with significant bleeding.
- Symptoms included epistaxis (nosebleeds), conjunctival hemorrhage, and bilateral periorbital ecchymosis (bruising around the eyes).
Findings:
- The infant's presentation suggests a potential diagnosis of Kasabach-Merritt syndrome.
- This highlights the diverse clinical manifestations of KMS in infants.
- Early recognition of bleeding symptoms is crucial for timely diagnosis.
Implications:
- This case underscores the importance of considering KMS in infants with unexplained bleeding and vascular tumors.
- Prompt diagnosis and management are vital to prevent severe complications.
- Further research into the pathogenesis and treatment of KMS is warranted.