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Granulomatosis with polyangiitis-associated acute subglottic stenosis in a 13-year-old boy: a case report
Giuliana Geng-Ramos1, Nina Nami2, David J Mener3
1Division of Pediatric Anesthesia, Department of Anesthesiology and Critical Care Medicine, Johns Hopkins Hospital, Baltimore, MD, USA. ggengra1@jhmi.edu.
Insights
This case study details the anesthetic management of a child with granulomatosis with polyangiitis presenting with subglottic stenosis and acute respiratory distress.
Area of Science:
- Pediatric Anesthesiology
- Rheumatology
- Pulmonology
Background:
- Granulomatosis with polyangiitis (GPA) is a rare autoimmune vasculitis that can affect the upper and lower respiratory tracts.
- Subglottic stenosis is a serious complication of GPA, potentially leading to airway obstruction and respiratory failure.
- Anesthetic management in pediatric patients with GPA and subglottic stenosis requires careful planning to mitigate risks.
Observation:
- A pediatric patient with known GPA presented with acute respiratory distress.
- The respiratory distress was attributed to severe subglottic stenosis.
- The case highlights the challenges in managing the airway in such patients.
Findings:
- Successful anesthetic management was achieved for a pediatric patient with GPA and subglottic stenosis.
- The anesthetic approach focused on securing the airway while minimizing trauma and exacerbation of stenosis.
- Potential complications, including bleeding and airway injury, were carefully monitored and managed.
Implications:
- This case underscores the importance of a multidisciplinary approach in managing pediatric patients with GPA and airway compromise.
- It provides insights into safe anesthetic techniques for complex airway scenarios in pediatric rheumatology patients.
- Early recognition and intervention for subglottic stenosis in GPA are crucial for favorable outcomes.
Abstract:
We present a case of a child with granulomatosis with polyangiitis, admitted with acute respiratory distress attributed to subglottic stenosis. The anesthetic management and potential complications are described.
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