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Updated: Mar 16, 2026
Step-by-Step Stapedotomy through Transcanal Exclusive Endoscopic Approach
Published on: March 5, 2022
Stapedectomy in Teunissen-Cremers Syndrome: Intraoperative Findings and Hearing Outcomes
Alice C Coombs1, Philip A Bird
1*Department of Otolaryngology Head and Neck Surgery, Dunedin Hospital, Dunedin †Department of Otolaryngology Head and Neck Surgery, Christchurch Hospital, Christchurch, New Zealand.
Objective:
To describe the intraoperative findings and outcomes of stapedectomy surgery in Teunissen-Cremers syndrome.
Patients:
A family of three patients with bilateral conductive hearing loss because of Teunissen-Cremers syndrome.
Intervention:
Six exploratory tympanotomies and stapedectomies, including one revision operation.
Main Outcome Measures:
Intraoperative findings and postoperative hearing results.
Results:
There was an increased distance between the incus and the vestibule, a thicker long process of the incus, and slight variation in the relative position of the ossicles in all patients. Surgery resulted in closure of the air-bone gap to less than 10 dB in all five operated ears.
Conclusion:
We describe anatomic abnormalities of the ossicular chain in Teunissen-Cremers syndrome. Prosthesis availability should include prostheses that can adapt to these potential anatomic abnormalities. Stapedectomy resulted in good long-term hearing outcomes in this series.
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