[Congenital broncho-biliary fistula: a case report]
Cinthia G Pérez1, Aixa Reusmann2,
1Servicio de Endoscopía Respiratoria, Hospital de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad de Buenos Aires, Argentina. cinthiagperezent@gmail.com.
Archivos Argentinos De Pediatria
|September 9, 2016
Summary
Congenital bronchobiliary fistula is a rare condition where the airway connects to the bile ducts. Early diagnosis and surgical repair are crucial for survival in affected neonates.
Area of Science:
- Medical Science
- Pediatric Surgery
- Gastroenterology
Background:
- Congenital tracheo-or-bronchobiliary fistula (CBBF) is a rare malformation with high morbidity and mortality.
- It involves an abnormal communication between the respiratory and biliary tracts, with only 35 cases reported globally.
- Early diagnosis is critical for improving outcomes in neonates presenting with this condition.
Observation:
- A neonate presented with right-sided pneumonia and bilious fluid in the endotracheal tube.
- Bronchoscopy combined with fluoroscopy was utilized for accurate diagnosis of the fistula.
- The presence of bile duct hypoplasia necessitated further surgical intervention.
Findings:
- A congenital bronchobiliary fistula was identified in a neonate.
- Surgical intervention included videothoracoscopy to resect the fistula.
- A left hepatectomy with Roux-en-Y biliary-digestive anastomosis was performed due to associated bile duct hypoplasia.
Implications:
- This case highlights the importance of early diagnosis and prompt surgical management of CBBF.
- Successful surgical repair can significantly improve the prognosis for neonates with this rare condition.
- The management strategy may involve a combination of airway and hepatobiliary procedures.
