Related Experiment Video
Updated: Mar 15, 2026
04:55
Author Spotlight: Simulating Pediatric Cardiac Surgery Using a Neonatal Piglet Model
Published on: May 26, 2023
1.5K
Modified pediatric Bentall procedure: A novel technique in a rare case
Gananjay G Salve1, Satish R Javali1, Bharat V Dalvi1
1Department of Pediatric Cardiovascular and Thoracic Surgery, Seven Hills Hospital, Marol-Maroshi Road, Andheri East, Mumbai, India.
Annals of Pediatric Cardiology
|September 15, 2016
Summary
Pediatric ascending aortic aneurysms are rare, often linked to Marfan syndrome. A novel Bentall procedure modification successfully treated a 4-year-old with Loeys-Dietz syndrome, showing promising short-term results.
Area of Science:
- Cardiovascular Surgery
- Pediatric Cardiology
- Genetics
Background:
- Ascending aortic aneurysms are uncommon in children, with Marfan syndrome being a rare associated condition.
- The standard surgical approach for pediatric aortic root pathology is the Bentall procedure.
Observation:
- A 4-year-old male presented with a large ascending aortic aneurysm, aortic root dilation, and severe aortic regurgitation.
- The patient exhibited phenotypic characteristics consistent with Loeys-Dietz syndrome type I.
Findings:
- The child underwent a modified Bentall procedure utilizing a medial trap-door technique for coronary reimplantation.
- This novel surgical modification yielded encouraging short-term outcomes.
Implications:
- This case highlights a potentially effective surgical modification for complex aortic root aneurysms in pediatric patients with connective tissue disorders.
- The medial trap-door technique may offer a viable alternative for coronary reimplantation in challenging pediatric cases.
- Further research and long-term follow-up are warranted to establish the broader applicability and durability of this technique.
