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[Thibièrge-Weissenbach syndrome].
1Handchirurgischen Abteilung der Oststadtklinik Mannheim.
Handchirurgie, Mikrochirurgie, Plastische Chirurgie : Organ Der Deutschsprachigen Arbeitsgemeinschaft Fur Handchirurgie : Organ Der Deutschsprachigen Arbeitsgemeinschaft Fur Mikrochirurgie Der Peripheren Nerven Und Gefasse : Organ Der V
|July 1, 1989
Summary
This case study details a patient with Thibièrge-Weissenbach syndrome, a rare scleroderma form. Recurring digital calcifications necessitated ten surgeries over eleven years.
Area of Science:
- Dermatology
- Rheumatology
- Surgical Pathology
Background:
- Thibièrge-Weissenbach syndrome is a rare, progressive scleroderma variant.
- Characterized by extensive calcifications, particularly in the digits.
- This condition poses significant therapeutic challenges due to recurrence.
Observation:
- A female patient presented with recurrent calcifications in her fingers.
- The condition necessitated multiple surgical interventions over an extended period.
- The case highlights the progressive and debilitating nature of the syndrome.
Findings:
- Ten surgical operations were required over eleven years to manage recurring digital calcifications.
- The case underscores the persistent and invasive nature of calcific deposits in Thibièrge-Weissenbach syndrome.
- Detailed pathology of the condition is presented.
Implications:
- Effective management strategies for Thibièrge-Weissenbach syndrome require further investigation.
- Understanding the pathology is crucial for differentiating from other connective tissue diseases.
- This case contributes to the limited literature on surgical management of digital calcifications in scleroderma variants.