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[Thibièrge-Weissenbach syndrome].

E Scharizer1

  • 1Handchirurgischen Abteilung der Oststadtklinik Mannheim.

Handchirurgie, Mikrochirurgie, Plastische Chirurgie : Organ Der Deutschsprachigen Arbeitsgemeinschaft Fur Handchirurgie : Organ Der Deutschsprachigen Arbeitsgemeinschaft Fur Mikrochirurgie Der Peripheren Nerven Und Gefasse : Organ Der V
|July 1, 1989
PubMed
Summary

This case study details a patient with Thibièrge-Weissenbach syndrome, a rare scleroderma form. Recurring digital calcifications necessitated ten surgeries over eleven years.

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Area of Science:

  • Dermatology
  • Rheumatology
  • Surgical Pathology

Background:

  • Thibièrge-Weissenbach syndrome is a rare, progressive scleroderma variant.
  • Characterized by extensive calcifications, particularly in the digits.
  • This condition poses significant therapeutic challenges due to recurrence.

Observation:

  • A female patient presented with recurrent calcifications in her fingers.
  • The condition necessitated multiple surgical interventions over an extended period.
  • The case highlights the progressive and debilitating nature of the syndrome.

Findings:

  • Ten surgical operations were required over eleven years to manage recurring digital calcifications.
  • The case underscores the persistent and invasive nature of calcific deposits in Thibièrge-Weissenbach syndrome.
  • Detailed pathology of the condition is presented.

Implications:

  • Effective management strategies for Thibièrge-Weissenbach syndrome require further investigation.
  • Understanding the pathology is crucial for differentiating from other connective tissue diseases.
  • This case contributes to the limited literature on surgical management of digital calcifications in scleroderma variants.

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