[A case of idiopathic myointimal hyperplasia of mesenteric veins]
Aurélie Cauchois1, Véronique Desfourneaux2, Solène-Florence Kammerer-Jacquet1
1Service d'anatomie pathologique, hôpital Pontchaillou, CHU de Rennes, 2, rue Henri-Le-Guilloux, 35000 Rennes, France.
Abstract:
The idiopathic myointimal hyperplasia of mesenteric veins is a rare pathology, affecting recto-sigmoid and mimicking clinically an inflammatory chronic disease of the bowel. Only about fifteen cases have been reported in the literature. This lesion is characterized by a myointimal thickening of the mesenteric veins, without inflammatory infiltrate of the vascular wall, differentiating it from vasculitis. We present here the case of a 48-year-old man, in whom the diagnosis of ulcerative colitis then digestive vasculitis had first been raised.
Insights
Idiopathic myointimal hyperplasia of mesenteric veins is a rare condition affecting the bowel. This case highlights its distinct vascular thickening, differentiating it from inflammatory bowel disease and vasculitis.
Area of Science:
- Vascular pathology
- Gastroenterology
- Rare diseases
Background:
- Idiopathic myointimal hyperplasia of mesenteric veins is a rare condition.
- It affects the recto-sigmoid region and clinically mimics chronic inflammatory bowel disease.
- Few cases (around 15) have been documented.
Observation:
- The lesion is characterized by myointimal thickening of mesenteric veins.
- Crucially, there is no inflammatory infiltrate within the vascular wall.
- This histological feature distinguishes it from vasculitis.
Findings:
- A case report of a 48-year-old male patient is presented.
- Initial diagnoses considered were ulcerative colitis and digestive vasculitis.
- The patient's condition was ultimately diagnosed as idiopathic myointimal hyperplasia of mesenteric veins.
Implications:
- This case underscores the importance of considering rare vascular pathologies in the differential diagnosis of chronic bowel conditions.
- Accurate diagnosis relies on differentiating vascular thickening from inflammation.
- Further research into idiopathic myointimal hyperplasia of mesenteric veins is warranted to improve diagnostic and treatment strategies.
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