Simultaneous occurrence of intussusception and duodenal haematoma in a patient with Glanzmann's thrombasthenia

Iftikhar Ahmad Jan1, Saif Khalfan AlKaabi2, Awadh AlMughadam3

  • 1Department of Pediatric Surgery, Zayed Military Hospital, Abu Dhabi, United Arab Emirates.

Glanzmann's thrombasthenia (GT) is a rare autosomal recessive disorder in which the platelets have anomalies of fibrinogen receptors causing bleeding tendencies. The disease usually presents with mucosal bleeding, petechial haemorrhages or gastrointestinal (GI) bleeding. Only sporadic cases of intussusception or duodenal haematoma have been reported with GT. We present a case of 5-year-old girl admitted with non-bilious vomiting, watery diarrhoea and abdominal pain. She is a known patient of Glanzmann's thrombasthenia.

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