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[A case of successful modified Fontan operation in pulmonary atresia and intact ventricular septum]
[Zasshi] [Journal]. Nihon Kyobu Geka Gakkai
|June 1, 1989
Insights
A 5-year-old girl with pulmonary atresia underwent a successful modified Fontan operation. This definitive procedure addressed her hypoplastic right ventricle and tricuspid valve, despite prior interventions.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease Surgery
- Cardiac Physiology
Background:
- Pulmonary atresia with intact ventricular septum is a complex congenital heart defect.
- Previous palliative surgeries (Brock, shunt) may not fully address ventricular hypoplasia.
- Hypoplastic tricuspid valve presents a significant challenge in surgical management.
Abstract:
A 5 year-old girl with pulmonary atresia with intact ventricular septum underwent a modified Fontan operation successfully. In spite of the previous Brock and shunt procedures, the right ventricle remained hypoplastic as end diastolic volume of 50% of normal with hypoplastic tricuspid valve. A modified Fontan operation was performed as a definitive operation with main reason of hypoplastic tricuspid valve. The selection of the definitive procedures was discussed.