[The Gottron syndrome from the dentist's viewpoint, case report].

Area of Science:

• Medical Genetics
• Dermatology
• Oral and Maxillofacial Surgery

Background:

• Gottron's syndrome is a rare condition characterized by specific dermatological and physical manifestations.
• Understanding its full spectrum, including dental and craniofacial anomalies, is crucial for accurate diagnosis.

Observation:

• The study observed facultative changes in dentition, oral structures, and the jaw in patients with Gottron's syndrome.
• Associated symptoms included acrogeria, acromicria, and facial erythema.

Findings:

• Specific dental findings noted were hypoplasia of the jaw and altered teeth positioning.
• Disproportionate vertical facial dimensions were also identified, consistent with syndrome characteristics.

Implications:

• Early recognition of these craniofacial and dental signs can aid in the diagnosis of Gottron's syndrome.
• Comprehensive evaluation including dental and facial assessments is recommended when Gottron's syndrome is suspected.