A retroperitoneal extra-renal wilms' tumour: A case report
S Wabada1, A S Abubakar2, A I Adamu3
1Paediatric Surgery Unit, Department of Surgery, University of Maiduguri Teaching Hospital, Maiduguri. Borno State, Nigeria.
Nigerian Journal of Clinical Practice
|March 4, 2017
Summary
Extra-renal Wilms' tumour is rare, presenting as an abdominal mass. Histology confirmed the diagnosis in a 2-year-old boy, showing it may not differ from typical intra-renal cases.
Area of Science:
- Pediatric oncology
- Nephrology
- Surgical pathology
Background:
- Wilms' tumour (nephroblastoma) typically arises from kidney tissue.
- Extra-renal Wilms' tumour (ERWT) is rare, accounting for 0.5-1% of cases.
- Diagnosis of ERWT is challenging based solely on clinical and radiological findings.


