[Quadricuspid Aortic Valve with Atrial Septal Defect;Report of a Case]

The patient was a 69-year-old man who had 1st experienced exertional dyspnea approximately 1 month earlier. He visited our hospital for treatment because his symptoms had gradually worsened and he had developed orthopnea. Echocardiography revealed an atrial septal defect(ASD) and a quadricuspid aortic valve with moderate regurgitation. As patch closure of the ASD alone could pose a risk of exacerbating the untreated aortic regurgitation, we performed both procedures patch closure and aortic valve replacement through median sternotomy concomitantly. The postoperative course was favorable. We report our experience with a rare case of quadricuspid aortic valve with ASD and a review the relevant literature.