[When an encircling aortic arch anomaly hides behind respiratory and digestive symptoms in children]

M Solowianiuk1, C Soulatges2, N Farhat3

  • 1Pédiatrie, Université de Liège, Belgique.

Insights

Congenital aortic arch anomalies, a common heart defect, can cause airway and esophageal compression. Surgical correction effectively resolved symptoms in two pediatric cases, highlighting the importance of early diagnosis.

Area of Science:

  • Cardiovascular Surgery
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Aortic arch anomalies represent 15-20% of congenital cardiovascular malformations.
  • These anomalies can lead to significant airway and esophageal compression, presenting with symptoms like dysphagia, stridor, and recurrent respiratory infections.

Observation:

  • Two pediatric cases of encircling aortic arch anomaly are presented.
  • One patient, a 3-year-old boy, experienced chronic respiratory issues since infancy. The other, a 20-month-old boy, had intermittent stridor, dysphagia, and vomiting.

Findings:

  • Cervico-thoracic CT-scans revealed a right aortic arch with a retro-esophageal left subclavian artery and Kommerell's diverticulum in both children.
  • Surgical intervention proved curative for both patients.

Implications:

  • Early diagnosis and treatment of aortic arch anomalies are crucial.
  • Understanding embryological development and recognizing clinical signs of vascular compression are essential for effective management.

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