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Vaterian cancer in siblings
J C Austin1, C H Organ, G R Williams
1Department of Surgery, University of Oklahoma Health Sciences Center, Oklahoma City 73126.
Annals of Surgery
|June 1, 1988
Summary
Familial Vaterian carcinoma, a rare pancreatic cancer, occurred in two siblings, suggesting a genetic predisposition. This highlights a potential inherited cancer syndrome manifesting as periampullary malignancy.
Area of Science:
- Gastroenterology
- Oncology
- Genetics
Background:
- Vaterian carcinoma, a rare malignancy, presents with obstructive jaundice and weight loss.
- Simultaneous occurrence in siblings suggests a potential genetic link.
- Exclusion of familial polyposis coli and Gardner's syndrome in affected individuals.