Related Experiment Videos
Gorham's disease in humerus treated with autogenous vascularized fibular graft
Jeung Woo Kim1, Hong Je Kang1, Dong Chul Kim2
1Department of Orthopaedic Surgery, School of Medicine, Wonkwang University, Iksan, Korea.
Insights
Gorham's disease, a rare bone disorder causing massive osteolysis, presents diagnostic and treatment challenges. This case highlights successful surgical management of a humerus fracture with a vascularized fibular graft.
Area of Science:
- Orthopedics
- Rare bone diseases
- Skeletal pathology
Background:
- Gorham's disease, also known as massive osteolysis, is a rare idiopathic bone disorder.
- It is characterized by progressive bone resorption and replacement by vascular, fibrous tissue.
- Diagnosis is challenging, often retrospective, with no standardized treatment protocols.
Purpose of the Study:
- To report a case of Gorham's disease presenting as a pathologic humerus fracture in an adolescent male.
- To describe the surgical management and long-term outcome of this rare condition.
- To contribute to the limited literature on Gorham's disease treatment.
Main Methods:
- Case presentation of an 18-year-old male with a humerus shaft fracture.
- Diagnosis of Gorham's disease confirmed after presentation.
- Surgical intervention involving wide excision of affected bone and reconstruction with an autogenous vascularized fibular graft.
Main Results:
- Successful surgical treatment of the pathologic humerus fracture.
- No recurrence or major complications observed during the 10-year follow-up period.
- Restoration of limb function and structural integrity.
Conclusions:
- Gorham's disease requires individualized treatment approaches.
- Autogenous vascularized fibular grafting can be an effective reconstructive option for Gorham's disease involving long bone fractures.
- Long-term follow-up is crucial for managing this rare condition.
Abstract:
Gorham's disease is a rare disorder of the bone characterized by progressive massive osteolysis. The pathophysiology is unknown, and diagnosis is often difficult. Most cases are often recognized retrospectively. There is no standardized treatment and management for Gorham's disease. We report a case of an 18-year-old male presenting with a pathologic fracture in the humerus shaft diagnosed with Gorham's disease. Patient was treated with autogenous vascularized fibular graft with wide excision and a 10 years followup after first surgery.