Primary Synovial Sarcoma of the Orbit

Area of Science:

• Ophthalmology
• Oncology
• Pathology

Background:

• Primary orbital synovial sarcoma is an exceptionally rare malignancy.
• Synovial sarcoma typically affects the extremities but can occur in the orbit.

Observation:

• A 6-year-old female presented with orbital synovial sarcoma.
• Diagnosis was confirmed via pathological examination and immunohistochemistry.
• The tumor involved the lateral orbital and temporal regions.

Findings:

• Surgical resection of the orbital tumor was performed.
• The patient received 5 cycles of chemotherapy.
• Initial one-year follow-up showed no evidence of tumor recurrence.

Implications:

• This report highlights a rare pediatric case of orbital synovial sarcoma.
• Successful treatment involved a multimodal approach including surgery and chemotherapy.
• Further research into pediatric orbital malignancies is warranted.